Pathobiology of Rare Lung Diseases

ISBN-13: 9780128243824 / Angielski / Miękka / 2024

Cormac McCarthy; Francesco Bonella

Spis treści

Part 1. Genetic Causes of Lung Disease
1. Genetics of Fibrotic Lung Disease
2. Multigene Familial ILD
3. Monogenic

Part 2. Disorders of Surfactant Homeostasis
1. Primary pulmonary alveolar proteinosis
2. Secondary pulmonary alveolar proteinosis
3. Disorders of surfactant production

Part 3. Childhood Interstitial Lung Diseases
1. Alveolar capillary dysplasias
2. Pulmonary interstitial glycogenosis
3. Neuroendocrine hyperplasia of infancy
4. Lung growth abnormalities

Part 4. Disorders Associated with Autoimmunity and Inflammation
1. Rheumatoid arthritis associated lung disease
2. Systemic sclerosis associated lung disease
3. Myositis associated disorders
4. IgG4-related Lung Disease
5. Anti-glomerular basement disease
6. Pulmonary manifestations of vasculitis
7. Pulmonary amyloidosis
8. Cryptogenic organizing pneumonia
9. Hypersensitivity pneumonitis
10. Sarcoidosis

Part 5. Neoplastic Disorders
1. Lymphangioleiomyomatosis
2. Pulmonary Langerhans cell histiocytosis
3. Diffuse idiopathic pulmonary neuroendocrine hyperplasia (DPNECH)

Part 6. Smoking-associated ILD
1. Desquamative interstitial pneumonia
2. Respiratory-bronchiolitis ILD
3. Combined pulmonary fibrosis and emphysema

Part 7. Pulmonary Complications of Rare Diseases
1. Primary immunodeficiencies
2. Sickle cell disease
3. Congenital diaphragmatic hernia
4. Lymphatic anomalies
5. Yellow nail syndrome
6. Pulmonary arterial hypertension